{"id":2419,"date":"2026-01-28T12:11:49","date_gmt":"2026-01-28T10:11:49","guid":{"rendered":"https:\/\/www.kliinikum.ee\/harvikhaigused\/?p=2419"},"modified":"2026-01-28T12:11:52","modified_gmt":"2026-01-28T10:11:52","slug":"progresseeruv-perekondlik-intrahepaatiline-kolestaas-pfic-ja-alagillei-sundroom-esinemissagedus-vastavalt-1-50-000-100-000-ja-1-30-000-ravim-on-nuud-eestis-patsientidele-huvita","status":"publish","type":"post","link":"https:\/\/www.kliinikum.ee\/harvikhaigused\/progresseeruv-perekondlik-intrahepaatiline-kolestaas-pfic-ja-alagillei-sundroom-esinemissagedus-vastavalt-1-50-000-100-000-ja-1-30-000-ravim-on-nuud-eestis-patsientidele-huvita\/","title":{"rendered":"Progresseeruv perekondlik intrahepaatiline kolestaas (PFIC) ja Alagille\u2019i s\u00fcndroom, esinemissagedus vastavalt 1: 50 000-100 000 ja 1: 30 000 \u2013 ravim on n\u00fc\u00fcd Eestis patsientidele h\u00fcvitatav!"},"content":{"rendered":"\n<p class=\"wp-el\">Nii perekondlik intrahepaatiline kolestaas kui Alagille`i s\u00fcndroom viivad m\u00f5lemad sapphappe kuhjumiseni organismis, mis omakorda tekitab edasisi probleeme. Neist t\u00f5siseim on raskekujuline maksakahjustus, kuid ka igap\u00e4evaelu tugevalt h\u00e4iriv intensiivne s\u00fcgelus.<\/p>\n\n\n\n<p class=\"wp-el\">Alates 1. jaanuarist 2026 on ravim Kayfanda (odeviksibaat) Eestis nende n\u00e4idustuste korral patsientidele h\u00fcvitatav. Ravimi toimeaineks on odeviksibaat, mis on selektiivne sapphappe transporteri inhibiitor. See aitab kaasa sapphappe eemaldamisele organismist ning seel\u00e4bi v\u00e4heneb sapphappe kuhjumisest tingitud intensiivne s\u00fcgelus ning maksakahjustuse teke aeglustub. Ravim parandab oluliselt patsientide elukvaliteeti ja on n\u00e4idustatud alates 6 kuu vanusest. Ravim on kapslite kujul, mida tarvitatakse suukaudselt, vajadusel v\u00f5ib kapsleid avada ning sisu segada toidu v\u00f5i vedelikuga.<\/p>\n","protected":false},"excerpt":{"rendered":"<p>Nii perekondlik intrahepaatiline kolestaas kui Alagille`i s\u00fcndroom viivad m\u00f5lemad sapphappe kuhjumiseni organismis, mis omakorda tekitab edasisi probleeme. Neist t\u00f5siseim on&#8230;<\/p>\n","protected":false},"author":9,"featured_media":0,"comment_status":"closed","ping_status":"closed","sticky":false,"template":"","format":"standard","meta":{"_acf_changed":false,"inline_featured_image":false,"advgb_blocks_editor_width":"","advgb_blocks_columns_visual_guide":"","footnotes":"","_links_to":"","_links_to_target":""},"categories":[1],"class_list":["post-2419","post","type-post","status-publish","format-standard","hentry","category-uudised"],"acf":[],"featured_image_src":null,"author_info":{"display_name":"Kristi R\u00e4hn","author_link":"https:\/\/www.kliinikum.ee\/harvikhaigused\/author\/kristisi\/"},"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v27.5 - https:\/\/yoast.com\/product\/yoast-seo-wordpress\/ -->\n<title>Progresseeruv perekondlik intrahepaatiline kolestaas (PFIC) ja Alagille\u2019i s\u00fcndroom, esinemissagedus vastavalt 1: 50 000-100 000 ja 1: 30 000 \u2013 ravim on n\u00fc\u00fcd Eestis patsientidele h\u00fcvitatav! - Harvikhaigused<\/title>\n<meta name=\"robots\" content=\"index, follow, max-snippet:-1, max-image-preview:large, max-video-preview:-1\" \/>\n<link rel=\"canonical\" href=\"https:\/\/www.kliinikum.ee\/harvikhaigused\/progresseeruv-perekondlik-intrahepaatiline-kolestaas-pfic-ja-alagillei-sundroom-esinemissagedus-vastavalt-1-50-000-100-000-ja-1-30-000-ravim-on-nuud-eestis-patsientidele-huvita\/\" \/>\n<meta property=\"og:locale\" content=\"et_EE\" \/>\n<meta property=\"og:type\" content=\"article\" \/>\n<meta property=\"og:title\" content=\"Progresseeruv perekondlik intrahepaatiline kolestaas (PFIC) ja Alagille\u2019i s\u00fcndroom, esinemissagedus vastavalt 1: 50 000-100 000 ja 1: 30 000 \u2013 ravim on n\u00fc\u00fcd Eestis patsientidele h\u00fcvitatav! - Harvikhaigused\" \/>\n<meta property=\"og:description\" content=\"Nii perekondlik intrahepaatiline kolestaas kui Alagille`i s\u00fcndroom viivad m\u00f5lemad sapphappe kuhjumiseni organismis, mis omakorda tekitab edasisi probleeme. 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